Zbornik je sestavljen iz dveh vsebinskih delov. Prvi del so zbrana dela študentov medicine, v katerih predstavijo specifike različnih področij od prenatalne diagnostike, rokovanja z novorojenci, prizadetosti organskih sistemov do sodobnih pristopov zdravljenja cistične fibroze. V drugem delu so zbrani povzetki predavanj s kongresa. Slavka Grmek Ugovšek predstavi Društvo za cistično fibrozo Slovenije, Alja Klara Ugovšek deli osebno izkušnjo življenja s cistično fibrozo. Vključena so predavanja strokovnjakov z različnih področij pediatrije: dr. Maja Tomazin - pulmologija, dr. Jernej Brecelj - gastroenterologija, Lidija Skočir - respiratorna fizioterapija. Z vidika interne medicine nam spregovorita dr. Matjaž Fležar in dr. Barbara Salobir o zdravljenju in življenju s cistično fibrozo. Pripravo na presaditev pljuč ter presaditev pljuč pa predstavita dr. Matjaž Turel in dr. Tomaž Štupnik.

Background. The clinical electroretinogram is a flash-evoked potential of the retina recorded by surface electrodes. The electroretinography is a noninvasive and objective examination which has been - nonstandardised - in clinical practice for many years. International Society for Clinical Electrophysiology of Vision (ISCEV) wishes to standardise electroretinographicexamination and had therefore published parameters, which should be considered in laboratories to record more comparable results. Aim ofthis study was to record first electroretinographic responses according to ISCEV standards at the University Institute for Clinical Electrophysiology, totest the recommended procedures and mode of examination with the elaborationof normative values. This will enable the laboratory to accept the standardised examination in its routine clinical practice. We also tested a new laboratory produced non-corneal HK-loop electrode. Methods. Electroretinograms (ERGs) were performed in 40 healthy volunteers and 12 patients with retinitis pigmentosa. As active electrodes we used non-corneal HK-loop electrodes. The preparation of patients as well as parameters of the electroretinographic system were adjusted according to the ISCEV standards. Results obtained in a group of volunteers produced normative electroretinographic data. The electroretinographic responses of patients withretinitis pigmentosa were compared with those obtained in healthy volunteers. Conclusions. The method proved to be efficient in electrophysiological evaluation of retinal function. Our volunteers and patients reported the non-corneal HK-loop electrode comfortable and we find itstable and sensitive enough for reliable flash ERG recording. Variability ofthe ERG signals recorded with HK-loop electrode was approximately in the same range as reported with corneal electrodes. (Abstract truncated at 2000 characters).